Asian Journal of Research and Reports in Ophthalmology

Cystoid Macular Edema in Retinitis Pigmentosa Patients and its Medical Management: A Case Report

Manal Bouggar *

Department of Ophthalmology, Mohammed V Military Hospital, Mohammed V University of Rabat, Morocco.

Houda Brarou

Department of Ophthalmology, Mohammed V Military Hospital, Mohammed V University of Rabat, Morocco.

Zakaria Chaibi

Department of Ophthalmology, Mohammed V Military Hospital, Mohammed V University of Rabat, Morocco.

Yassine Mouzari

Department of Ophthalmology, Mohammed V Military Hospital, Mohammed V University of Rabat, Morocco.

Abdelbare Oubaaz

Department of Ophthalmology, Mohammed V Military Hospital, Mohammed V University of Rabat, Morocco.

*Author to whom correspondence should be addressed.

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Abstract

Retinitis Pigmentosa (RP) take in a group of hereditary retinopathies that lead to  progressive vision loss ; RP may be complicated by cystoid macular oedema (CMO). A 40-year-old  female presented with fluctuant blurred vision for 4 years. Best corrected Visual acuity (BCVA) was 20/20 in both eyes. Examination and imaging showed besides  bone spicule pigmentation  a  macular edema . Currently the patient is under medical treatement. Successful management of RP-CMO should allow to improve  quality and quantity of vision in the short term and also slow the progression of  central vision loss on the long term. This report describes a case of using carbonic anhydrase inhibitor CAI per os medication to manage CMO secondary to RP in a long term.

Keywords: Retinitis pigmentosa, macular edema, carbonic anhydrase inhibitor, vision loss

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